Jan 5, Portal cavernoma (PC) is the most critical condition with risk or variceal hemorrhage in pediatric patients. We retrospectively investigated the. Cavernous transformation of the portal vein (also called portal cavernoma) occurs when the native portal vein is thrombosed and myriads of collateral channels. La obstrucción de la vena porta con un hígado sano es una causa frecuente de hipertensión portal en los niños. El curso natural de la enfermedad se.

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In most of the patients, the liver functions were satisfactory; the high portal vein pressure is the prominent problem to control.

Furthermore, we found that the presence of ascites was another important prognostic factor for the posttreatment recurrent variceal bleeding. You can also scroll through stacks with your mouse wheel or the keyboard arrow keys.

Although the recurrent variceal bleeding was demonstrated with high prevalence in our patients, the post-medical intervention death was not so prominent only one patient died of massive variceal bleedingwhich could be explained by the advances in bleeding control and long-term liver function maintenance [ 21 — 23 ]. The degree of ascites was divided into heavy, medium, and modicum under the CDUS evaluation.

The therapeutic strategy was to gain the maximal beneficial effects of symptom resolution with minimal invasiveness. After the age of 18 these patients are referred to and managed by gastroenterologists. Pathology Radiographic features Treatment and prognosis References Images: What is the procedure for taking admission in NIOS? The patients were treated conservatively and, at the present moment, remain symptom-free.


Platelet count; fibrinogen; prothrombin time; esophageal varices; portal cavernoma. Based on the importance of ascites in pediatric patients with portal cavernoma, therapeutic decision making needs to be altered according to the presence of ascites [ 20 ].

Home: The National Institute of Open Schooling (NIOS)

Additionally, these patients would be excluded if they were receiving experimental treatment trial or were unable to have regular hepatic function assessments. In this study, we performed a retrospective cohort study to evaluate the outcome of pediatric patients with portal cavernoma and measure predictors of recurrent variceal bleeding after medical intervention. MRI is also a proven method for imaging the portal venous system and may be used as a complementary or alternative modality to CT.

The clinical records were thoroughly collected upon admission or referral. Eur J Ultrasound, 8pp.

Cavernlmatosis total of patients were enrolled in the study. Up to now, the totally agreed upon guidelines for this disease are unavailable, and therapeutic options vary in different centers; when these fail, further medical options are limited, especially for intrahepatic cavernoma. The treatments and their effectiveness were evaluated for each portao. State Bank Colony, G. Click here to see all Subjects Available. Technical Support Mail Us: Several cases exhibited severe dilated blood vessels in the lower esophagus and under the gastric fundic mucosa with lumpy, tortuous of the lumen of the lower esophagus and lumpy protuberance in the gastric cavity Figure 1 a.

At the time of analysis, eligible and evaluable patients diagnosed with portal cavernoma without liver cirrhosis or abdominal malignancy fulfilled the nioos for inclusion in our study. From January to Julyconsecutive patients with confirmed diagnosis of portal cavernoma were enrolled in this observational study.

What is the eligibility criteria for admission to the Secondary Course? The presence of severe ascites, collateral circulation, and high portal venous pressure remained significant in the logistic regression model and so were regarded as independent predictors of recurrent variceal bleeding in pediatric patients with portal cavernoma Table 5. Dilated and tortuous portal vein cavernoma. A comparison of patients with and without postprocedural recurrent variceal bleeding is given in Table 4.


The minimum age to take admission in the Secondary Course is 14 years as on 31st July born on or before A valid proof of Residence like Aadhaar Card with complete address printed on it, valid Passport etc.

Evaluation with CT and MR imaging.

Therefore, the current conclusions should be adopted cautiously and confirmed in larger research in the future. Following the splenectomy and gastric fundic and lower esophageal vascular disconnection, no severe hematemesis recurrence or obvious black tarry feces pirtal in 33 pediatric patients.

Gastroenterology Research and Practice

Slow blood flow through this tortuous network of veins, redistribution of the blood, and new thromboses all contribute to the increase of nioos vein pressure [ 2 — 4 ]. To our knowledge, this is the largest study to describe prognostic information and the csvernomatosis of portal cavernoma patients in pediatrics. It is therefore important that gastroenterologists become aware of the fact that, in long-term survivors who have undergone the variceal hemorrhage operation, complications such as recurrent variceal hemorrhage and portal hypertension may occur.

Eur J Pediatr,pp. Case 3 Case 3.